Inflammatory Linear Verrucous Epidermal Nevus is a rare disease of the skin that presents as multiple, discrete, red papules that tend to coalesce into linear plaques that follow the Lines of Blaschko. The plaques can be slightly warty (psoriaform) or scaly (eczema-like). ILVEN is caused by somatic mutations that result in genetic mosaicism. There is no cure, but different medical treatments can alleviate the symptoms.
この患者は、生後5か月のときに頭皮の右前部に黄色い斑点が出現しました。6か月になると、頭皮の右側後部に色素沈着した疣贅状の丘疹が形成されました。過去5年間、これらの斑点はゆっくりと拡大しましたが、顔の右側、頭皮、首に限局しています。痛みやかゆみはなく、成長は順調です。右頬と額にはわずかに隆起した黄色の斑点があり、頭皮の前面と側面に広がっています。これらの斑点は、色素沈着が過剰な疣贅状の丘疹と連続しており、頭皮の後部から右側の首の後方にかけて線状に分布しています。 The patient first showed up at five months old with yellow patches on the right front of the scalp. By six months, they had hyperpigmented verrucous papules on the back right side of the scalp. Over the past five years, these spots slowly grew bigger but stayed only on the right side of the face, scalp, and neck. They aren't painful or itchy, and the patient is growing normally. The right cheek and forehead have slightly raised, yellow patches that stretch onto the front and side of the scalp. Connected to these patches are hyperpigmented, verrucous papules, forming lines from the back of the scalp to the back of the neck on the right side.
○ 診断と治療
いぼと形状が似ているため、鑑別が必要です。表皮母斑はレーザー切除により除去できます。